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Journal of Paediatric Surgeons of Bangladesh
Case Reports · Vol. 14 No. 1-2 (2023)

Adult Presentation of Untreated Exstrophy–Epispadias Complex with Squamous Cell Carcinoma: A Rare Case Report

Vol. 14 No. 1-2 (2023) — cover
Cover
JPSB
Journal of
Paediatric Surgeons of Bangladesh
Published : July 2023
CONTENTSVolume 14Number 1 & 2January - July 2023
Editorial
Gender Diversity and Disorders of Sex Development: Time for Greater Medical Awareness in Bangladesh
Md Nazrul Islam
01
Original Articles
Impact of Prematurity and Low Birth Weight on Postoperative Mortality in Neonatal Intestinal Obstruction
Manash Talukdar, Md Tawhidul Islam, Shabnam Rashedi, Dibendu Kumar Das, Md Tayef Rahman, Must Tamanna Ruksana, Towkir Ahmed, Anshua Das Trisha
04
Early intervention in NTDs in children leads to better surgical outcome
Anupam Das, Mohammad Mahabubul Alam
11
Use of Pavlik Harness in the Treatment of Infantile Femur Fracture: Clinical and Radiological Outcome
Tafhim Ehsan Kabir, Touhidul Islam, Rahma Binte Anwar, Nafeesa Mubashshira
17
Assessing the Role of Mid-day Meal (MDM) on the Nutritional Profile of School Going Children: Snapshot of a Suburban School
Arpita Biswangree, Md Fahadul Islam, Mustari Nailah Tabassum, Rahatil Asyekin Raha, Sakibul Alam, Mohammad Ismail, Md Sharif Imam, Tahmina Banu
24
Operational Diagnostic Criteria in Conjunction with the Triangular Cord Sign Enhance the Screening for Biliary Atresia
Md Jahidur Rahman, Manash Talukdar Talukdar, Md Mahbub Hossain, Shabnam Rashedi, Sabrina Rahman Mahi
31
Penile Agenesis: Demographic Characteristics and Management Experience in a Tertiary Care Teaching Hospital in Bangladesh
Md Nazrul Islam, Shoheli Alam, Mohammad Mahbubul Alam, Taslima Akter, Asma Ul Husna, Sabrina Khan Mou, Pravin Chowdhury, Mohammad Idrish Ali
36
Evaluation of Chronic Gingivitis in Response to Nickel Chromium and Gold Alloy Crown
Mohammadullah, Md Nazrul Islam, Mohammed Mahbub Zaki, Tawfiqur Rahman, Md Immamur Rashid, Mohammad Idrish Ali
39
Congenital choanal atresia - Endonasal endoscopic surgery - Bangabandhu Sheikh Mujib Medical University
Mohammad Idrish Ali, Kamrul Hasan Tarafder, Sheikh Hasanur Rahman, Rokeya Begum, Md Nazrul Islam, Asma Ul Husna, Sabrina Khan Mou
45
Case Reports
Adult Presentation of Untreated Exstrophy–Epispadias Complex with Squamous Cell Carcinoma: A Rare Case Report
Md Ruhul Amin, Md Nazrul Islam, Pravin Chowdhury
49
The Official Journal of the
ASSOCIATION OF PAEDIATRIC SURGEONS OF BANGLADESH (APSB)
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Authors

  • Md Ruhul AminProfessor, Department of Paediatric Surgery, BSMMU, Dhaka, Bangladesh.
  • Md Nazrul IslamDepartment of Paediatric Surgery, BSMMU, Dhaka, Bangladesh.
  • Pravin ChowdhuryResident, Department of Paediatric Surgery, BSMMU, Dhaka, Bangladesh

Keywords

Exstrophy–epispadias complex adult presentation bladder exstrophy squamous cell carcinoma radical cystectomy Mitrofanoff procedure

Abstract

Exstrophy–epispadias complex (EEC) is a rare congenital anomaly characterized by a midline defect of the lower abdominal wall involving the urinary bladder, external genitalia, and pelvic bones. Early diagnosis and surgical reconstruction in the neonatal period is the standard of care. Untreated cases persisting into adulthood are extremely uncommon and are associated with a significant risk of malignant transformation of the exposed bladder mucosa. We report a rare case of untreated exstrophy–epispadias complex in a 38-year-old male who presented with an ulcerated bladder plate that was subsequently diagnosed as invasive squamous cell carcinoma. The patient underwent organ-sparing radical cystectomy with continent urinary diversion using an ileocecal segment and a Mitrofanoff catheterizable channel, along with epispadias repair and umbilicoplasty. Histopathology confirmed grade II invasive squamous cell carcinoma with tumor-free surgical margins. This case highlights the importance of early diagnosis and treatment of bladder exstrophy and demonstrates the potential for malignant transformation in long-standing untreated cases.

Journal of Paediatric Surgeons of Bangladesh (2023) Vol. 14 (1 & 2): 49–51

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