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Association of Paediatric Surgeons of Bangladesh
Journal of Paediatric Surgeons of Bangladesh
Case Reports · Vol. 1 No. 1 (2010)

Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome – A Case Report

Cover
JPSB
Journal of
Paediatric Surgeons of Bangladesh
Published : January 2010
CONTENTSVolume 01Number 1January 2010
Editorial
Pediatric Surgery – Challenging Speciality in SAARC Region
Devendra K Gupta
03
Review Articles
Revival of Landing's Concept of Infantile Obstructive Cholangiopathy – A Plea to Hand Over the 2 Week Old Jaundiced Full Term Neonate to the Surgeon!
Shilpa Sharma, Devendra K Gupta
37
Postoperative Results Following Surgery for PUJO in Children
Prabudh Goel, Devendra K Gupta
53
Original Articles
Laparoscopically Assisted Anorectoplasty Using Perineal Ultrasonographic Guide
Akio Kubota
06
Laparoscopic Pyeloplasty - Our Early Experience
Gazi Mohammad Zakir Hossain, Mofizur Rahman, Rashedul Hasan
10
A Prospective Comparative Study of the Outcome of Double-Y Pyloromyotomy (Alayet's Pyloromyotomy) and Ramstedt's Pyloromyotomy for the Surgical Management of Infantile Hypertrophic Pyloric Stenosis
Md. Ansar Ali, Md. Sharifuzzaman, Md. Ashraf Ul Huq, Md. Mahbub-Ul Alam
15
Extradural Haematoma in Children: Surgical Experiences and Prospective Analysis of 138 Cases
Sharif Md. Noman Khaled Chowdhury, Abdul Hanif, K M Tarikul Islam, Ehsan Mahmud, Sk. Sader Hossain
19
Evaluation of the Outcome of IRPG 910 and Polypropylene in Terms of Cosmesis and Cost for Skin Closure in Cleft lip Surgery
Md. Akbar Hossain Bhuiyan, Shahanara Chowdhury, Shafiqul Hoque
25
Neonatal Surgery: Demand and Survival Both are Increasing: Eight Years Experience in Dhaka Medical College Hospital, Bangladesh
Abdul Hanif, Kaniz Hasina, Ahmed Zahid Hossain, S M Shamsul Huda, M Kamrul Hassan, Md. Mahbub-Ul Alam, AKM Zahid Hossain
30
Miscellaneous
Neonatal Surgery
Anette Jacobsen
65
Case Reports
Mayer-Rokitansky-Kuster-Hauser (MRKH) Syndrome – A Case Report
Md. Kabirul Islam, Md. Shah Alam, Abdul Hanif, Md. Kamrul Hasan, Mizanur Rahman
70
Endoscopic Removal of Vesical Calculus Through Suprapubic Route: A Case Report
Md. Akbar Hossain Bhuyian, Md. Ashraf Ul Huq, Mahfuzul Kabir, Shafquat Haider Chowdhury
74
Two Case Reports of Peutz Jegher's Syndrome
Abdul Hanif, Kaniz Hasina, Md. Kamrul Hassan, Shah Alam Talukder, Md. Kabirul Islam
77
Ambiguous Genitalia with Perineal Rhabdomyosarcoma: A Case Report
Tahmina Banu, Tanvir Kabir Chowdhury, Md. Mozammel Hoque
80
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ASSOCIATION OF PAEDIATRIC SURGEONS OF BANGLADESH (APSB)
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Authors

  • Md. Kabirul IslamDepartment of Pediatric Surgery, Square Hospitals Ltd, Dhaka
  • Md. Shah AlamDepartment of Pediatric Surgery, Dhaka Medical College Hospital, Dhaka
  • Abdul HanifDepartment of Pediatric Surgery, Dhaka Medical College Hospital, Dhaka
  • Md. Kamrul HasanDepartment of Pediatric Surgery, Dhaka Medical College Hospital, Dhaka
  • Mizanur RahmanDepartment of Pediatric Surgery, Bangabandhu Sheikh Mujib Medical University, Dhaka

Keywords

MRKH vaginal malformation

Abstract

We report a case of Mayer-Rokitansky-Kuster-Hauser (MRKH) syndrome in a 25 year old married lady. Though it is a congenital abnormality, she presented as primary infertility after 2 year of her marriage and was referred to us from a Gynaecologist. She had absent vagina, rudimentary uterus with no cervix. Her ovaries were severely hypoplastic. The anus was placed anteriorly and opened into the vulva. In spite of absence of her vagina, the lady somehow maintained her married life by doing intercourse through the anteriorly placed rectum. The vagina was made from the lower end of existing rectum which opened into the vulva. The proximal end of the rectum and left colon were pulled through the pelvis and opened into the perineum. It improved her quality of life.

Journal of Paediatric Surgeons of Bangladesh (2010) Vol. 1 (1): 70–73

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